WebDec 11, 2014 · Pulmonary alveolar proteinosis (PAP) is a rare disease characterized by alveolar accumulation of surfactant. PAP results of defective surfactant clearance by alveolar macrophages. Diagnosis of PAP is evoked by CT scan and confirmed by staining of bronchoalveolar lavage fluid (BALF) or transbronchial biopsies. Diagnosis rarely requires … WebChronic pulmonary disease characterized by filling of alveoli by eosinophilic proteinaceous fluid; Alternate/Historical Names. Pulmonary alveolar phospholipoproteinosis; Alveolar …
Pulmonary alveolar proteinosis presenting with pneumothorax
WebDec 12, 2024 · Pulmonary alveolar proteinosis (PAP) is a rare syndrome frequently described erroneously as a single disease. These disorders are marked by dysregulated production and/or inadequate clearance of surfactant. Abnormalities in granulocyte–macrophage colony stimulating factor signalling are implicated in the … WebOriginal Article from The New England Journal of Medicine — Pulmonary Alveolar Proteinosis Skip to main ... which is of necessity no more than an outline. ... Path. 26: 787 –793, 1956. Crossref; hope this helpful for you
Pulmonary alveolar proteinosis
WebAutoimmune pulmonary alveolar proteinosis (aPAP) is a rare autoimmune lung disorder. It is the most common form (90% of the cases) of pulmonary alveolar proteinosis (PAP). … WebAug 21, 2024 · Definition / general. Rare disease with accumulation of acellular surfactant presumedly due to impaired clearance, likely due to dysfunction of alveolar macrophages. Considered a response to alveolar injury, not a specific entity. Congenital (2% of cases), … clinical pathology. More than 4,500 textbook topics are organized by chapter … Advertise Your Pathology Fellowships With Us! All fellowship ads appear for one year … Page views in 2024 to date (this page and chapter topics): 123,446 NTRK gene fusions can be detected using various testing methods, including NGS, … Monthly Statistics at PathologyOutlines - Pathology Outlines - Alveolar proteinosis Testis & Paratestis - Pathology Outlines - Alveolar proteinosis Salivary Glands - Pathology Outlines - Alveolar proteinosis Oral Cavity & Oropharynx - Pathology Outlines - Alveolar proteinosis WebApr 12, 2024 · GM-CSF-deficient mice developed pulmonary alveolar proteinosis (PAP) as a major phenotype, although steady-state myelopoiesis changed minimally. GM-CSF is reportedly required for the development of alveolar macrophages via the induction of peroxisome-proliferator-activated receptor (PPAR)-γ expression, while macrophage … long step exercise