WebPhenylketonuria (PKU) is a rare genetic mutation of the phenylalanine hydroxylase enzyme which results in high phenylalanine levels. The enzyme requires vitamin C, tetrahydrobiopterin, and iron as cofactors. The mainstay of treatment involves a low-protein diet, cofactor support, and the use of a phenylalanine-free formulas. WebNov 21, 2024 · Nuts (almonds, walnuts, hazelnuts, etc.) Seeds: In particular, pumpkin seeds and sunflower seeds contain a lot of phenylalanine Fruits and vegetables are low in phenylalanine. Other sources of phenylalanine There are other sources of this amino acid to consider: – Protein supplements or hyperproteic supplements
Low Phenylalanine Foods - Medindia
WebFeb 20, 2012 · The objective of this study was to identify urinary metabolite profiles that discriminate between high and low intake of dietary protein during a dietary intervention. Seventy-seven overweight, non-diabetic subjects followed an 8-week low-calorie diet (LCD) and were then randomly assigned to a high (HP) or low (LP) protein diet for 6 months. … WebSEM and CGM mainly affect phenylalanine and tyrosine metabolism. Phenylalanine is a precursor of tyrosine biosynthesis . Metabolome data showed that the phenylalanine content in muscle was significantly higher than the FM group while the tyrosine content was significantly lower than the FM group which was consistent with amino acid composition ... terry white chemmart mooroopna
PKU Diet: What to Eat For Better Management
WebJul 8, 2011 · This includes cod, crab, lobsters, mussels, oysters, tuna, salmon and sardines. Meat, being a high-protein food, is also high in phenylalanine, in many cases containing more phenylalanine per serving than fish. Bacon, beef, turkey, liver, chicken and gelatin all contain over 1 gram of phenylalanine per 3 ounce serving. Eggs and Dairy WebOct 31, 2024 · What to Eat. Medical foods, shakes, powders designed for PKU. Most fruits and fruit juices. Most non-starchy vegetables (and juices) Low protein breads and pastas. Fats like olive oil, butter, margarine, … WebJun 22, 2012 · Phenylketonuria (pronounced fen-l-kee-toh-NOOR-ee-uh ), often called PKU, is an inherited disorder that that can cause intellectual and developmental disabilities … terry white chemmart parklands